Pulmonary Atresia with Intact Ventricular Septum: Management Options and Decision-making

Pulmonary atresia with intact ventricular septum (PA-IVS) is a complex congenital heart malformation with a diverse set of anatomical and clinical findings. The incidence is 4.1 per 100,000 live births and is less than 1% of all congenital heart disease. During embryogenesis, PA-IVS is postulated to occur after development of ventricular septum which is later than the development of PA with ventricular septal defect. Every case of PA-IVS poses a considerable challenge to the pediatric cardiologist and cardiovascular surgeon. Although echocardiography is often the first line tool in cardiac imaging, cardiac catheterization is the gold standard for diagnosing PA-IVS and describing the important anatomical features that determine the plan of treatment. This article will focus on the management options and decision making from the interventional cardiologists point of view. *Corresponding author: Henry Burkholder, Division of Pediatric Cardiology, University of Texas Houston Medical School, 6410 Fannin Street, UTPB–425, Houston, TX 77030, USA, Tel: 713-500 5738; Fax: 713-500 5751; E-mail: [email protected] Received February 21, 2012; Accepted December 17, 2012; Published December 19, 2012 Citation: Burkholder H, Balaguru D (2012) Pulmonary Atresia with Intact Ventricular Septum: Management Options and Decision-making. Pediat Therapeut S5:007. doi:10.4172/2161-0665.S5-007 Copyright: © 2012 Burkholder H, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.